806 Artículos relativos a Esfingolípidos

• Enzymatic abnormalities in diseases of sphingolipid metabolism.
  Publicado en Clin Chem
• Sphingolipid metabolism in leukemic leukocytes.
  Publicado en Cancer Res
• Sphingolipid metabolism in neural tissues.
  Publicado en Neurosci Res (N Y)
• Further developments in studies in sphingolipidoses: "missing enzymes".
  Publicado en Riv Patol Nerv Ment
• Biochemische Differenzierung der Mucopolysaccharidosen.
  Publicado en Monatsschr Kinderheilkd
• The genetic mucolipidoses.
  Publicado en Neuropadiatrie
• Cerebral lipid composition during myelination in murine genetic leukodystrophies.
  Publicado en Neurology
• Progresos recientes sobre la esfingolipidosis.
  Publicado en Minerva Pediatr
• Chemistry of glycosphingolipids Fabry's disease.
  Publicado en Chem Phys Lipids
• Analisi strutturale di glicerofosfatidi e sfingolipidi mediante la gas-cromatografia e la spettrometria di massa.
  Publicado en Ann Ist Super Sanita
• Determination of the structure of sphinga-4,8-dienine from oyster glycolipids by gas chromatography and mass spectrometry.
  Publicado en Biochim Biophys Acta
• Glycosphingolipids and amines in neoplastic mast cells.
  Publicado en Biochem Pharmacol
• The lipid class composition of Semliki forest virus and plasma membranes of the host cells.
  Publicado en Virology
• Recent advances in the cerebromacular degenerations.
  Publicado en J Natl Med Assoc
• Cattle blood group J glycolipid. I. Isolation and identification of the trihexoside ceramide component of J hapten.
  Publicado en Immunochemistry
• Glycolipid synthesis in the early prereplicative phase of isoproterenol-stimulated salivary glands of mice.
  Publicado en J Biol Chem
• Development of abnormal lipid bodies in various sphingolipidoses.
  Publicado en Proc Soc Exp Biol Med
• The J blood-group substance of cattle. Studies in animals with J substance in serum and erythrocytes and animals with J substance only in serum.
  Publicado en Eur J Biochem
• A convenient procedure for the synthesis of ceramides.
  Publicado en J Lipid Res
• Studies in the sphingolipids series. XXXII. Synthesis and resolution into optical antipodes of C 20 -phytosphingosine.
  Publicado en Chem Phys Lipids
• Biosynthesis of glycosphingolipids by mouse neuroblastoma (NB41A), rat glia (RGC-6) and human glia (CHB-4) in cell culture.
  Publicado en Biochem Biophys Res Commun
• Sphingolipids.
  Publicado en Annu Rev Biochem
• The lipid composition of the blood of marine mammals. II. Atlantic bottlenose dolphins, Tursiops truncatus and two species of seals, Halichoerus grypus and Phoca vitulina.
  Publicado en Comp Biochem Physiol B
• Abnormality in sphingolipid fatty acids from sciatic nerve and brain of Quaking mice.
  Publicado en J Neurochem
• Genetic disorders of myelination. In: lipids, malnutrition & the developing brain.
  Publicado en Ciba Found Symp
• Thin-layer chromatography of red cell glycosphingolipids from various mammalian species.
  Publicado en J Chromatogr
• A new approach for determining red cell life span by incorporating C 14 -glucose into glycosphingolipids of membrane.
  Publicado en J Lab Clin Med
• Quantitative analysis of lipid classes.
  Publicado en Am J Clin Nutr
• the central nervous system in Fabry's disease. A clinical, pathological, and biochemical investigation.
  Publicado en Arch Neurol
• Lipid patterns in human leukocytes maintained in long-term culture.
  Publicado en J Lipid Res
• Identification of heterozygous carriers of lipid storage diseases. Current status and clinical applications.
  Publicado en Am J Med
• Serum phospholipids in neoplastic disorders.
  Publicado en Clin Chim Acta
• The association of the galactosyl diglycerides of brain with myelination. II. The inability of the myelin-deficient mutant, jimpy mouse, to synthesize galactosyl diglycerides effectively.
  Publicado en J Biol Chem
• Evidence for a terminal -D-galactopyranosyl residue in galactosylgalactosylglucosylceramide from human kidney.
  Publicado en J Biol Chem
• Disorders of lipid metabolism--sphingolipidoses.
  Publicado en Shinkei Kenkyu No Shimpo
• Fucosidose.
  Publicado en Monatsschr Kinderheilkd
• The fatty acid composition of phospholipids and glycolipids in Jimpy mouse brain.
  Publicado en J Neurochem
• Kletochnye membranes.
  Publicado en Biofizika
• The binding of botulinum toxin to membrane lipids: sphingolipids, steroids and fatty acids.
  Publicado en J Neurochem
• Fatty acid composition of cerebrosides, sulphatides and ceramides in murine sudanophilic leucodystrophy: the Jimpy mutant.
  Publicado en J Neurochem
• Analogous reactions for the biosynthesis of monosialo- and disialo-gangliosides in brain.
  Publicado en J Biol Chem
• Lactosylceramidosis: lactosylceramide galactosyl hydrolase deficiency and accumulation of lactosylceramide in cultured skin fibroblasts.
  Publicado en J Pediatr
• Quaking mouse: in vitro studies of brain sphingolipid biosynthesis.
  Publicado en Brain Res
• Characterization of cerebroside sulfotransferase from rat brain.
  Publicado en J Biol Chem
• Splenic transplantation in a case of Gaucher's disease.
  Publicado en Lancet
• Brain sphingoglycolipids in Krabbe's globoid cell leucodystrophy.
  Publicado en J Neurochem
• Biosynthesis of sphingolipid bases. IV. The biosynthetic origin of sphingosine in Hansenula ciferri.
  Publicado en Arch Biochem Biophys
• Fucosidosis: a glycosphingolipidosis.
  Publicado en N Engl J Med
• Ceramides in a patient with lipogranulomatosis (Farber's disease) with chronic course.
  Publicado en Scand J Clin Lab Invest
• Separation and identification of cerebrosides in cerebrospina fluid by gas chromatography--mas spectrometry.
  Publicado en Scand J Clin Lab Invest
• Identification and quantitative determination of ceramides in human plasma.
  Publicado en Scand J Clin Lab Invest
• The storage cells of chronic myelogenous leukemia.
  Publicado en Lab Invest
• The quantitative analysis of sphingolipids by determination of long chain base as the trinitrobenzene sulfonic acid derivative.
  Publicado en Lipids
• Pathologic lysosomes and increased urinary glycosylceramide excretion in Fabry's disease. Studies on a family with evidence of linkage with the sex-linked blood group Xg.
  Publicado en Lab Invest
• Isolation of glucosylceramides from yeast (Hansenula ciferri).
  Publicado en J Biol Chem
• Stereochemistry of the hydroxylation in 4-hydroxysphinganine formation and the steric course of hydrogen elimination in sphing-4-enine biosynthesis.
  Publicado en J Biol Chem
• Urinary screening of globoid-cell leukodystrophy.
  Publicado en N Engl J Med
• Comparison of cerebral sphingolipid metabolism in vivo in "quaking" and normal mice.
  Publicado en Life Sci II
• Anomeric structure of globoside and ceramide grihexoside of human erythrocytes and hamster fibroblasts.
  Publicado en J Biol Chem
• Characterization of the phospholipids and the normal and hydroxy acid containing glycosphingolipids (globosides) of pig erythrocytes.
  Publicado en Biochim Biophys Acta
• Quantitative isolation of total glycosphingolipids from animal cells.
  Publicado en J Lipid Res
• Glycosphingolipids in the spleen of developing rats.
  Publicado en J Lipid Res
• Composition of human cerebrospinal fluid cerebroside.
  Publicado en J Lipid Res
• Abnormality of cerebral neutral lipids and glycolipids in a case of Tay-Sachs disease which appeared in siblings.
  Publicado en Jpn J Exp Med
• Confirmation of linkage of the loci for myotonic dystrophy and ABH secretion.
  Publicado en J Med Genet
• Les Sphingolipidoses.
  Publicado en Arch Fr Pediatr
• The susceptibility of some complex sphingoglycolipids to -N-acetylhexosaminidase from hog epididymis.
  Publicado en J Biochem (Tokyo)
• Occurrence of long-chain fatty acids and glycolipids in the cell envelope fractions of baker's yeast.
  Publicado en Biochem J
• Sphingolipid biosynthesis by particulate fractions of normal and "quaking" mouse brain.
  Publicado en Lipids
• Isolation of a new sphingophosphonolipid containing galactose from the viscera of Turbo cornutus.
  Publicado en Biochim Biophys Acta
• Metabolism of sphingosine bases. XVII. Stereospecificities in the introduction of the 4t-double bond into sphinganine yielding 4t-sphingenine (sphingosine).
  Publicado en Hoppe Seylers Z Physiol Chem
• Vitamin K stimulation of sphingolipid synthesis.
  Publicado en Biochem Biophys Res Commun
• Ensignements apportés par ll'étude de la myélinisation chez des mutants de Souris.
  Publicado en C R Seances Soc Biol Fil
• On the phospholipids of Culex pipiens fatigans.
  Publicado en Lipids
• Four antigenic variants of blood group A glycolipid: examples of highly complex, branched chain glycolipid of animal cell membrane.
  Publicado en Biochem Biophys Res Commun
• Brain lipids.
  Publicado en Adv Lipid Res
• Der klirschrote Fleck der Macula als Ausdruck einer Speicherkrankheit.
  Publicado en Klin Monatsbl Augenheilkd
• Biosynthesis of brain sphingolipids and myelin accumulation in the mouse.
  Publicado en Lipids
• The cerebral sphingolipidoses (metachromatic leucodystrophy and infantile amaurotic idiocy) as human inborn errors of metabolism.
  Publicado en Biochem J
• Disorders of lipid metabolism.
  Publicado en Biochem J
• Enzyme replacement therapy by renal allotransplantation in Fabry's disease.
  Publicado en N Engl J Med
• Cell surface antigens: the P and I blood group systems and some aspects of polyagglutinability.
  Publicado en Med Lab Technol
• Fabry's disease (ceramide trihexosidase deficiency): diagnostic confirmation by analysis of dental pulp.
  Publicado en Arch Oral Biol
• Lysosomale enzymopathieën.
  Publicado en Ned Tijdschr Geneeskd
• Protein-lipid interactions.
  Publicado en Ciba Found Symp
• Specific radioactive labeling of terminal n-acetylgalactosamine of glycosphingolipids by the galactose oxidase-sodium borohydride method.
  Publicado en J Lipid Res
• Quantity and fatty acyl composition of the glycosphingolipids of Gaucher spleen.
  Publicado en J Lab Clin Med
• Enzyme defects in the sphingolipidoses and their application to diagnosis.
  Publicado en Ann Clin Lab Sci
• Detection of glycosphingolipids in small samples of human tissue.
  Publicado en Ann Clin Lab Sci
• Plasma glycosphingolipids in lipid disorders.
  Publicado en Ann Clin Lab Sci
• Fatty chains of different lipid classes of Semliki forest virus and host cell membranes.
  Publicado en J Virol
• Degradation of sphingosine bases during acid hydrolysis of sphingomyelin, cerebroside or psychosine.
  Publicado en J Biochem (Tokyo)
• Sphingolipids and their precursors in human brain (normal and MS).
  Publicado en Z Neurol
• Studies on the glycosphingolipids of normal and virally transformed 3T3 mouse fibroblasts.
  Publicado en J Biol Chem
• Glycosphingolipids in cultured human skin fibroblasts. II. Characterization and metabolism in fibroblasts from patients with inborn errors of glycosphingolipid and mucopolysaccharide metabolism.
  Publicado en J Biol Chem
• Glycosphingolipids in cultured human skin fibroblasts. I. Characterization and metabolism in normal fibroblasts.
  Publicado en J Biol Chem
• Galactosylsphingosine galactosyl hydrolase. Partial purification and properties of the enzyme in rat brain.
  Publicado en J Biol Chem
• High pressure liquid chromatography of neutral glycosphingolipids.
  Publicado en Biochim Biophys Acta
• Lipid composition of subcellular fractions from rat testis.
  Publicado en Biochim Biophys Acta
• Les sphingolipidoses. biochimie et mécanismes enzymatiques.
  Publicado en Nouv Presse Med